Benz G, Willich E, Schärer K
Pediatr Radiol. 1976 Dec 15;5(2):86-92. doi: 10.1007/BF00975313.
Radiological findings of segmental renal hypoplasia are reported, based on the observation of 6 children aged between 8 and 14. The leading clinical symptom is arterial hypertension. Urinary tract infection and proteinuria are additional common findings. Cases with bilateral disease often have renal failure. The intravenous urogram shows unilateral or bilateral small kidneys with segmental renal scarring and transverse lobulation. In the pathological areas the calyces are ectatic or clubbed and their infundibulum is elongated. Vesico-ureteral reflux is frequent. In angiography the lobulated segments appear hypovascular. Diagnosis was verified by histological examination.
报告了节段性肾发育不全的放射学表现,基于对6名年龄在8至14岁儿童的观察。主要临床症状是动脉高血压。尿路感染和蛋白尿是另外常见的表现。双侧患病的病例常出现肾衰竭。静脉肾盂造影显示单侧或双侧小肾脏,伴有节段性肾瘢痕形成和横向分叶。在病理区域,肾盏扩张或呈杵状,其漏斗部延长。膀胱输尿管反流很常见。血管造影中,分叶状节段显示血供减少。诊断通过组织学检查得以证实。