Urasaki E, Tokimura T, Genmoto T, Yokota A
Department of Neurosurgery, University of Occupational and Environmental Health, Fukuoka.
Neurol Med Chir (Tokyo). 1999 Feb;39(2):169-73. doi: 10.2176/nmc.39.169.
A 17-year-old male presented with paroxysmal kinesigenic choreoathetosis (PKC) associated with frontotemporal arachnoid cyst. Xenon-133 single photon emission computed tomography detected a slight but equivocal decrease in regional cerebral blood flow in the vicinity of basal ganglia associated with the PKC episodes. PKC continued after surgical removal of the cyst but was well controlled by oral administration of carbamazepine. Whether the pathogenesis of symptomatic PKC was associated with the cortical lesion could not be determined in the present case.
一名17岁男性患者,表现为与额颞部蛛网膜囊肿相关的发作性运动诱发性舞蹈手足徐动症(PKC)。氙-133单光子发射计算机断层扫描检测到与PKC发作相关的基底节附近区域脑血流轻微但不明确的减少。囊肿手术切除后PKC仍持续存在,但口服卡马西平可得到良好控制。在本病例中,无法确定症状性PKC的发病机制是否与皮质病变有关。