McCarthy E F, Lietman S, Argani P, Frassica F J
The Johns Hopkins Hospital, Department of Pathology, Baltimore, MD 21287, USA.
Skeletal Radiol. 1999 Feb;28(2):100-3. doi: 10.1007/s002560050482.
Endovascular papillary angioendothelioma, also known as Dabska tumor, is a rare vascular neoplasm that usually involves the skin or subcutaneous tissue of children. There have been no reported cases of this lesion occurring in bone. We report a Dabska tumor in the distal femur of a 45-year-old woman who, clinically and radiologically, was felt to have an osteoid osteoma. Histologic study of the lesion showed a hemangioma with budding fronds of endothelial cells, a feature characteristic of the Dabska tumor. We feel that the lesion arose in a pre-existing hemangioma, a hypothesis suggested in a few other case reports. Endovascular papillary angioendothelioma is a low-grade malignant neoplasm, although only one patient has died due to this lesion. Our patient is asymptomatic without evidence of recurrence 1 year post curettage.
血管内乳头状血管内皮瘤，也称为达布斯卡瘤，是一种罕见的血管肿瘤，通常累及儿童的皮肤或皮下组织。尚无该病变发生于骨骼的报道。我们报告了一例发生在一名45岁女性股骨远端的达布斯卡瘤，该患者临床和放射学表现均被认为患有骨样骨瘤。对该病变的组织学研究显示为一个伴有内皮细胞芽状突起的血管瘤，这是达布斯卡瘤的特征性表现。我们认为该病变起源于一个先前存在的血管瘤，其他一些病例报告也提出了这一假说。血管内乳头状血管内皮瘤是一种低级别恶性肿瘤，尽管仅有1例患者因该病变死亡。我们的患者无症状，刮除术后1年无复发迹象。
