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[持续性脾-性腺融合:一例报告]

[Continuous splenic-gonadal fusion: a case report].

作者信息

Orellana M E, Oviedo-Ayala N

机构信息

Instituto Anatomopatológico Dr. José A. O'Daly, Facultad de Medicina, Universidad Central de Venezuela, Caracas, Venezuela.

出版信息

Invest Clin. 1999 Mar;40(1):67-73.

Abstract

Splenic-gonadal fusion is an extremely rare congenital anomaly that results from fusion between the splenic and gonadal anlage during embryonic development. Approximate 90 cases have been reported in the literature. The condition has been divided into two major groups: continuous splenic-gonadal fusion in which a continuous cord-like structure connects the spleen and the gonadal-mesonephric structure, and dis-continuous splenic-gonadal fusion in which no such connection exists. We report a case of continuous splenic-gonadal fusion in a 2 1/2 years old boy presenting a left inguinal mass and a right inguinal hernia. They were removed without complications.

摘要

脾-性腺融合是一种极其罕见的先天性异常,它是在胚胎发育过程中脾和性腺原基之间融合的结果。文献中已报道了约90例病例。这种情况主要分为两大类:连续性脾-性腺融合,即有连续的索状结构连接脾脏和性腺-中肾结构;以及非连续性脾-性腺融合,即不存在这种连接。我们报告了一例2岁半男孩的连续性脾-性腺融合病例,该患儿表现为左侧腹股沟肿块和右侧腹股沟疝。肿块和疝均被切除,未出现并发症。

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