Keitel W, Fuchs R, Weber G, Lutze G
Z Gesamte Inn Med. 1976 Dec 1;31(23):998-1000.
It is reported on the casuistics of a 23-year-old Lebanese who since his eighth year suffered from joint swellings and occasional attacks of jaundice. By the proof of false forms of erythrocytes and by the haemoglobin electrophoresis a homozygous sickle cell disease could be ascertained. Peculiarities of the clinical picture were among others changes of the bones of high degree (osteolyses of vertebral bodies, of the head of the right humerus and the heads of the two femurs) was well as of the knee-joints in form of ankyloses.
据报道,一名23岁的黎巴嫩人自8岁起就患有关节肿胀和偶尔的黄疸发作。通过对异常红细胞形态的检测以及血红蛋白电泳,确诊为纯合子镰状细胞病。临床表现的特点包括高度的骨骼变化(椎体、右肱骨头和双侧股骨头的骨质溶解)以及膝关节以强直性脊柱炎形式出现的变化。