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一名患有Sweet综合征男孩的心血管受累情况。

Cardiovascular involvement in a boy with Sweet's syndrome.

作者信息

Guia J M, Frias J, Castro F J, Gracián M

机构信息

Sección de Cardiologia Pediátrica, Hospital Infantil, "Virgen de la Arrixaca," Crta. Murcia-Cartagena s/n, El Palmar, 30120 Murcia, Spain.

出版信息

Pediatr Cardiol. 1999 Jul-Aug;20(4):295-7. doi: 10.1007/s002469900468.

DOI:10.1007/s002469900468
PMID:10368458
Abstract

Acute febrile neutrophilic dermatosis (Sweet's syndrome) is a rare disease in infancy. It may present in an isolated manner or be associated with diverse conditions. Only two children with postinflammatory slack skin who developed cardiovascular disease have been described to date, both of whom died from coronary artery occlusion. We report a boy with Sweet's syndrome and diffuse vascular disease involving the aorta and the supraaortic vessels, the pulmonary trunk, and the right coronary artery but without signs of coronary obstruction.

摘要

急性发热性嗜中性皮病(Sweet综合征)在婴儿期是一种罕见疾病。它可能以孤立的形式出现,或与多种病症相关。迄今为止,仅报道过两名患有炎症后皮肤松弛并发展为心血管疾病的儿童,两人均死于冠状动脉闭塞。我们报告一名患有Sweet综合征和弥漫性血管疾病的男孩,病变累及主动脉、主动脉弓血管、肺动脉干和右冠状动脉,但无冠状动脉梗阻迹象。

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[Sweet syndrome of childhood with acquired cutis laxa (Marshall syndrome) as primary manifestation of Takayasu arteritis].以获得性皮肤松弛(马歇尔综合征)为主要表现的儿童Sweet综合征作为Takayasu动脉炎的首发症状
Dermatologie (Heidelb). 2022 Nov;73(11):884-890. doi: 10.1007/s00105-022-04999-2. Epub 2022 Jul 15.
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Sweet's syndrome as a dermatological manifestation of underlying coronary artery disease.
Sweet综合征作为潜在冠状动脉疾病的一种皮肤表现。
J Cardiol Cases. 2012 Apr 10;6(1):e8-e12. doi: 10.1016/j.jccase.2012.03.002. eCollection 2012 Jul.
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Sweet heart: A case of pregnancy-associated acute febrile neutrophilic dermatosis with myopericarditis.甜心:一例伴有心肌炎的妊娠相关急性发热性嗜中性皮病。
JAAD Case Rep. 2014 Sep 30;1(1):12-4. doi: 10.1016/j.jdcr.2014.09.005. eCollection 2015 Jan.
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Sweet syndrome, cutis laxa, and fatal cardiac manifestations in a 2-year-old girl.一名2岁女童患Sweet综合征、皮肤松弛症及致命心脏表现
Tex Heart Inst J. 2011;38(3):285-7.
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Acute febrile neutrophilic dermatosis (Sweet's syndrome) in childhood and adolescence: two new patients and review of the literature on associated diseases.儿童及青少年急性发热性嗜中性皮病(斯威特综合征):两例新病例及相关疾病文献综述
Eur J Pediatr. 2009 Jan;168(1):1-9. doi: 10.1007/s00431-008-0812-0. Epub 2008 Sep 2.
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Sweet's syndrome--a comprehensive review of an acute febrile neutrophilic dermatosis.斯威特综合征——急性发热性嗜中性皮病的全面综述
Orphanet J Rare Dis. 2007 Jul 26;2:34. doi: 10.1186/1750-1172-2-34.