Guia J M, Frias J, Castro F J, Gracián M
Sección de Cardiologia Pediátrica, Hospital Infantil, "Virgen de la Arrixaca," Crta. Murcia-Cartagena s/n, El Palmar, 30120 Murcia, Spain.
Pediatr Cardiol. 1999 Jul-Aug;20(4):295-7. doi: 10.1007/s002469900468.
Acute febrile neutrophilic dermatosis (Sweet's syndrome) is a rare disease in infancy. It may present in an isolated manner or be associated with diverse conditions. Only two children with postinflammatory slack skin who developed cardiovascular disease have been described to date, both of whom died from coronary artery occlusion. We report a boy with Sweet's syndrome and diffuse vascular disease involving the aorta and the supraaortic vessels, the pulmonary trunk, and the right coronary artery but without signs of coronary obstruction.
急性发热性嗜中性皮病(Sweet综合征)在婴儿期是一种罕见疾病。它可能以孤立的形式出现,或与多种病症相关。迄今为止,仅报道过两名患有炎症后皮肤松弛并发展为心血管疾病的儿童,两人均死于冠状动脉闭塞。我们报告一名患有Sweet综合征和弥漫性血管疾病的男孩,病变累及主动脉、主动脉弓血管、肺动脉干和右冠状动脉,但无冠状动脉梗阻迹象。