Weinberg J, Doering C, McFarland E G
Long Island Jewish Medical Center, New Hyde Park, New York, USA.
Am J Orthop (Belle Mead NJ). 1999 Jul;28(7):406-9.
The Ehlers-Danlos syndrome (EDS) is a rare, hereditary, connective-tissue disorder that results in increased laxity and poor soft-tissue healing. Surgical results and complications in these patients are not well documented in the literature. The goal of the present study was to survey patients with EDS who had surgery to the musculoskeletal system and document the results of surgery and complications. Forty-four patients with EDS were surveyed regarding the complications and results of surgical procedures to the shoulder, the elbow, the knee, or the ankle. Surgical procedures were performed for pain, instability, poor range of motion, or a combination of these, totaling 214 procedures. The population surveyed in the present study demonstrates that problems of surgical procedures in EDS may be high relative to other populations without connective-tissue disorders. More study is warranted in this patient population to validate the results in a larger cohort.
埃勒斯-当洛综合征(EDS)是一种罕见的遗传性结缔组织疾病,会导致关节松弛加剧和软组织愈合不良。这些患者的手术结果和并发症在文献中记录得并不充分。本研究的目的是调查接受过肌肉骨骼系统手术的EDS患者,并记录手术结果和并发症。对44例EDS患者进行了调查,了解其肩部、肘部、膝部或踝部手术的并发症和结果。手术是针对疼痛、不稳定、活动范围不佳或这些情况的组合进行的,总共进行了214例手术。本研究中调查的人群表明,与其他无结缔组织疾病的人群相比,EDS患者手术的问题可能更高。有必要对这一患者群体进行更多研究,以在更大的队列中验证结果。