Al Jadaan S A, Al Rabeeah A
Department of Surgery, King Fahad National Guard Hospital, Riyadh, Saudi Arabia.
J Pediatr Surg. 1999 Jul;34(7):1130-2. doi: 10.1016/s0022-3468(99)90583-3.
Mesenteric fibromatosis is a rare, benign fibrous lesion found in the bowel mesentery or the retroperitoneum. Its biological behavior is intermediate between benign fibrous tissue proliferation and fibrosarcoma. Fibromatosis characteristically is locally invasive and tends to recur but does not metastasize. Most reported cases have been in older individuals, and there is a frequent association with familial polyposis coli, previous trauma, and hormonal imbalance. The authors report a case of mesenteric fibromatosis in a 32-month-old girl with a 1-month history of abdominal pain who was discovered to have an abdominal mass. After appropriate investigations, the mass was excised. The pathology report confirmed the diagnosis of fibromatosis. Mesenteric fibromatosis in children, as in adults, presents a management challenge for the surgeon.
肠系膜纤维瘤病是一种罕见的良性纤维性病变，见于肠系膜或腹膜后。其生物学行为介于良性纤维组织增生和纤维肉瘤之间。纤维瘤病的特征是具有局部侵袭性，易于复发但不转移。大多数报道的病例发生于老年人，并且常与家族性结肠息肉病、既往创伤和激素失衡有关。作者报告了一例32个月大女童的肠系膜纤维瘤病，该女童有1个月的腹痛病史，被发现腹部有肿块。经过适当检查后，切除了肿块。病理报告证实了纤维瘤病的诊断。儿童肠系膜纤维瘤病与成人一样，对外科医生来说是一个治疗难题。
