Radhakrishna V, Patil R S
Department Paediatric Surgery, Indira Gandhi Institute of Child Health, Bengaluru, India.
Department of General Surgery, Basaveshwar Hospital, MR Medical College, Gulbarga, India.
Kathmandu Univ Med J (KUMJ). 2017;15(60):350-351.
Mesenteric fibromatosis is a rare, locally invasive benign tumor arising from fibroblasts and fibrous tissue of mesentery. Their infiltrative nature can cause fatal visceral involvement. Most of the cases reported have an association with Gardner's Syndrome, prolonged intake of estrogen, and previous trauma, but mesenteric fibromatosis can occur as a primary ailment without an underlying stimulant. A nineteen-year female presented with mass and pain abdomen diagnosed to have subserous fibroid but eventually turned out to be primary mesenteric fibromatosis. She underwent wide excision along with the resection of adjacent bowel. She is on follow-up with no evidence of recurrence.
肠系膜纤维瘤病是一种罕见的、局部侵袭性的良性肿瘤,起源于肠系膜的成纤维细胞和纤维组织。其浸润性可导致致命的内脏受累。大多数报道的病例与加德纳综合征、长期摄入雌激素和既往创伤有关,但肠系膜纤维瘤病也可作为一种无潜在刺激因素的原发性疾病发生。一名19岁女性因腹部肿块和疼痛就诊,最初诊断为浆膜下肌瘤,但最终确诊为原发性肠系膜纤维瘤病。她接受了广泛切除及相邻肠段的切除。她正在接受随访,没有复发迹象。