Nishizaki K, Fukushiama K, Oda Y, Masuda A, Hayashi S, Nagayasu N, Yoshino T, Kashihara K, Takahashi K, Masuda Y
Department of Otorhinolaryngology, Okayama University Medical School, Japan.
Acta Otolaryngol Suppl. 1999;540:34-7.
Recently, the effectiveness of cochlear implantation for hereditary deafness has been reported. We performed cochlear implantation for two patients with symptomatic hereditary deafness. Deafness in one patient was thought to be a result of albinism-deafness syndrome and in the other patient, a result of chronic progressive external ophthalmoplegia syndrome. Since their speech perception abilities improved dramatically, we believe that cochlear implantation should be actively performed for these two syndromes.
最近，已有关于人工耳蜗植入治疗遗传性耳聋有效性的报道。我们为两名有症状的遗传性耳聋患者实施了人工耳蜗植入手术。其中一名患者的耳聋被认为是白化病 - 耳聋综合征所致，另一名患者的耳聋则是慢性进行性外眼肌麻痹综合征所致。由于他们的言语感知能力得到了显著改善，我们认为对于这两种综合征应积极开展人工耳蜗植入手术。
