儿童遗传性口形红细胞增多症脾切除术后门静脉血栓形成
Portal vein thrombosis after splenectomy for hereditary stomatocytosis in childhood.
作者信息
Perel Y, Dhermy D, Carrere A, Chateil J F, Bondonny J M, Micheau M, Barbier R
机构信息
Unité d'Onco-Hematologie Pediatrique, Hopital des Enfants, Centre Hospitalier et Universitaire de Bordeaux, France.
出版信息
Eur J Pediatr. 1999 Aug;158(8):628-30. doi: 10.1007/s004310051165.
UNLABELLED
Portal vein thrombosis is a rare but potentially lethal complication in children requiring splenectomy. We report on a 15-year-old boy with a dehydrated hereditary stomatocytosis, who underwent splenectomy and presented a postoperative partial portal vein thrombosis. With prompt heparin therapy, neither propagation of the thrombus nor further cavernous transformation in the following occurred 6 years.
CONCLUSION
Recent data suggest that hereditary stomatocytosis carries a high risk of thrombotic complications, especially after splenectomy. This procedure, the benefit of which is limited in this condition, should therefore be strongly avoided.
未标注
门静脉血栓形成是儿童脾切除术中一种罕见但可能致命的并发症。我们报告了一名15岁患有脱水遗传性口形红细胞增多症的男孩，他接受了脾切除术，术后出现部分门静脉血栓形成。经过及时的肝素治疗，血栓在接下来的6年中既没有扩展，也没有进一步发生海绵样变。
结论
最近的数据表明，遗传性口形红细胞增多症有很高的血栓形成并发症风险，尤其是在脾切除术后。因此，在这种情况下益处有限的该手术应强烈避免。
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