König M, Hentsch A, Schmieder K, Harders A, Heuser L
Department of Radiology and Nuclear Medicine, Ruhr University of Bochum, Knappschaftskrankenhaus Langendreer, In der Schornau 23/25, D-44892 Bochum, Germany.
Neuroradiology. 1999 Aug;41(8):579-83. doi: 10.1007/s002340050810.
Spinal dural arteriovenous fistulae are extremely rare in spinal dysraphism. A fistulous malformation within a lipomyelomeningocele has not been reported previously. A 50-year-old man presented with progressive paraparesis and bladder dysfunction. MRI revealed a large lumbar lipomyelomeningocele. A vascular malformation was indicated by abnormal signal in the thoracolumbar spinal cord and dilated perimedullary veins. Phase-contrast MRA demonstrated only the slow-flow veins of the fistula and an intradural ascending vein. Contrast-enhanced ultra-fast MRA gave excellent delineation of all parts of the fistula within the dysraphic lesion.
脊髓硬脊膜动静脉瘘在脊髓发育异常中极为罕见。脂肪脊髓脊膜膨出内的瘘管畸形此前未见报道。一名50岁男性出现进行性双下肢轻瘫和膀胱功能障碍。MRI显示一个巨大的腰部脂肪脊髓脊膜膨出。胸腰段脊髓异常信号及髓周静脉扩张提示存在血管畸形。相位对比磁共振血管造影仅显示瘘管的缓慢血流静脉和一条硬脊膜内上升静脉。对比增强超快磁共振血管造影能很好地显示发育异常病变内瘘管的各个部分。