Weon Y C, Chung J I, Roh H G, Eoh W, Byun H S
Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine, 50, llwon-Dong, Kangnam-Ku, Seoul, 135-710, Korea.
Neuroradiology. 2005 Oct;47(10):774-9. doi: 10.1007/s00234-005-1336-1. Epub 2005 Sep 1.
Combined spinal arteriovenous malformation and lipomyelomeningocele are extremely rare. We present a rare combined case of a lipomyelomeningocele with an intramedullary arteriovenous malformation (AVM) occurred at the L3-L4 level in a 30-year-old man who suffered from low back pain radiating to the lower extremities, dysuria, and frequency for 5 years. The MR studies showed an intradural mass with high-signal intensity on both T1-weighted and T2-weighted images, intermingled with multiple signal-void structures. The mass extended extradurally toward a subcutaneously forming fatty mass on the patient's back. Spinal angiography showed an AVM supplied by the radiculopial branches of the lumbar arteries and drained by tortuous, dilated, perimedullary veins. Endovascular embolization and surgical resection were performed.
脊髓动静脉畸形合并脂肪脊髓脊膜膨出极为罕见。我们报告了一例罕见的合并病例，一名30岁男性，L3 - L4水平发生脂肪脊髓脊膜膨出合并髓内动静脉畸形（AVM），患者有下背部疼痛并放射至下肢、排尿困难及尿频5年。磁共振成像（MR）研究显示硬膜内肿块在T1加权和T2加权图像上均呈高信号强度，夹杂多个无信号结构。肿块向硬膜外延伸至患者背部皮下形成脂肪团块。脊髓血管造影显示AVM由腰动脉的神经根软膜分支供血，并由迂曲、扩张的髓周静脉引流。进行了血管内栓塞和手术切除。
