Cione J A, Lynn B, Boylan J
Franciscan Health System of New Jersey, St. Mary Hospital, Hoboken, NJ 07030, USA.
J Am Podiatr Med Assoc. 1999 Aug;89(8):419-23. doi: 10.7547/87507315-89-8-419.
Dermatofibrosarcoma protuberans is a rare, slow-growing, locally destructive, intermediate-grade malignancy that originates in the dermal layer of the skin. Dermatofibrosarcoma protuberans rarely metastasizes and has a marked tendency to recur following local surgical excision. The lesion is found most commonly on the trunk, on the proximal aspect of both the lower and upper extremities, and in the head and neck region. Dermatofibrosarcoma protuberans occurs most commonly in people between the ages of 20 and 50. This article describes the clinical and pathologic features of this rare, malignant neoplasm and describes a rare case of dermatofibrosarcoma protuberans involving the pediatric foot.
隆突性皮肤纤维肉瘤是一种罕见的、生长缓慢、具有局部破坏性的中度恶性肿瘤,起源于皮肤的真皮层。隆突性皮肤纤维肉瘤很少发生转移,局部手术切除后有明显的复发倾向。该病变最常见于躯干、上下肢近端以及头颈部。隆突性皮肤纤维肉瘤最常发生于20至50岁的人群。本文描述了这种罕见恶性肿瘤的临床和病理特征,并介绍了一例累及小儿足部的隆突性皮肤纤维肉瘤罕见病例。