Vandeweyer E, Deraemaecker R, Somerhausen N D, Geledan L, Gebhart M
Surgery Department, Jules Bordet Institute Tumor Center of the Université Libre de Bruxelles, Brussels, Belgium.
Foot Ankle Int. 2001 Apr;22(4):339-41. doi: 10.1177/107110070102200412.
Pigmented dermatofibrosarcoma protuberans (Bednar tumor) is a rare neoplasm accounting for approximately 1-5% of all cases of dermatofibrosarcoma protuberans. The majority occurs on the trunk, and the remainders are more or less equally distributed in the upper and lower extremities and the head and neck. Microscopically it is characterized by spindled cells arranged in a tight storiform pattern and admixed with a small population of melanin-containing dendritic cells. The dendritic cells are the primary feature that distinguish this lesion from conventional dermatofibrosarcoma protuberans. We report here a case of Bednar tumor occurring on the dorsal aspect of the foot in a young female.
色素性隆突性皮肤纤维肉瘤（贝德纳瘤）是一种罕见肿瘤，约占所有隆突性皮肤纤维肉瘤病例的1 - 5%。大多数发生于躯干，其余病例在上、下肢以及头颈部的分布大致相等。显微镜下，其特征为梭形细胞呈紧密的席纹状排列，并混有少量含黑色素的树突状细胞。树突状细胞是将此病变与传统隆突性皮肤纤维肉瘤区分开来的主要特征。我们在此报告一例发生于年轻女性足部背侧的贝德纳瘤病例。
