Strobel J S, Fuisz A R, Epstein A E, Plumb V J
Division of Cardiovascular Disease, Department of Medicine, University of Alabama at Birmingham, Birmingham, Alabama 35294, USA.
J Interv Card Electrophysiol. 1999 Oct;3(3):225-9. doi: 10.1023/a:1009891406964.
Hemochromatosis has been associated with atrial tachyarrhythmias and congestive heart failure as a consequence of dilated or restrictive cardiomyopathy. Inducible ventricular fibrillation has not been previously described.
An electrophysiologic study was conducted in a woman after two episodes of syncope. Polymorphic ventricular tachycardia (PMVT) and ventricular fibrillation (VF) were induced with ventricular programmed stimulation. Magnetic resonance imaging demonstrated signal loss in the liver consistent with hemochromatosis, but normal cardiac size and function. Hematologic studies supported a diagnosis of hemochromatosis.
Cardiac hemochromatosis may be associated with serious ventricular arrhythmias.
血色素沉着症与心房快速性心律失常及扩张型或限制型心肌病导致的充血性心力衰竭有关。此前尚未有关于可诱导性室颤的描述。
对一名经历两次晕厥发作的女性进行了电生理研究。通过心室程控刺激诱发出多形性室性心动过速（PMVT）和室颤（VF）。磁共振成像显示肝脏信号缺失，符合血色素沉着症表现，但心脏大小和功能正常。血液学研究支持血色素沉着症的诊断。
心脏血色素沉着症可能与严重室性心律失常有关。
