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澳大利亚新南威尔士州慢性炎症性脱髓鞘性多发性神经病的患病率。

Prevalence of chronic inflammatory demyelinating polyneuropathy in New South Wales, Australia.

作者信息

McLeod J G, Pollard J D, Macaskill P, Mohamed A, Spring P, Khurana V

机构信息

Department of Medicine, University of Sydney and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital and the University of Sydney, New South Wales, Australia.

出版信息

Ann Neurol. 1999 Dec;46(6):910-3.

PMID:10589544
Abstract

A prevalence study of chronic inflammatory demyelinating polyneuropathy (CIDP) was performed in New South Wales (NSW), Australia, with a prevalence day of August 6, 1996, which coincided with a national census. The population of NSW was 5,995,544, and the crude prevalence of CIDP was 1.9 per 100,000 population. It was higher in male patients than in female patients, and the age-specific prevalence reached a maximum of 6.7 per 100,000 population in the 70- to 79-year-old age group. The prevalence in the city of Newcastle, with a population of 448,663, was 2.0 per 100,000 population and is representative of the whole of NSW. The estimated crude annual incidence was 0.15 per 100,000 population. The mean age of onset was 47.6 years (median, 53.5 years), 51% of patients had a relapsing-remitting course, the mean duration on prevalence day was 7.1 years (median, 5 years), and 87% of patients were able to walk without walking aids or other assistance.

摘要

1996年8月6日,澳大利亚新南威尔士州开展了一项慢性炎性脱髓鞘性多发性神经病(CIDP)患病率研究,该日恰逢全国人口普查。新南威尔士州人口为5995544人,CIDP的粗患病率为每10万人中有1.9例。男性患者的患病率高于女性患者,年龄别患病率在70至79岁年龄组达到最高,为每10万人中有6.7例。纽卡斯尔市人口为448663人,其患病率为每10万人中有2.0例,代表了整个新南威尔士州的情况。估计年粗发病率为每10万人中有0.15例。发病的平均年龄为47.6岁(中位数为53.5岁),51%的患者病程呈复发-缓解型,在患病率调查日的平均病程为7.1年(中位数为5年),87%的患者能够在无需助行器或其他辅助的情况下行走。

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