播散性黄瘤伴呼吸道受累及致命结局。
Xanthoma disseminatum with respiratory tract involvement and fatal outcome.
作者信息
Davies C W, Marren P, Juniper M C, Gray W, Wojnorowska F, Benson M K
机构信息
Osler Chest Unit, Churchill Hospital, Oxford Radcliffe Trust, Oxford OX3 7LJ, UK.
出版信息
Thorax. 2000 Feb;55(2):170-2. doi: 10.1136/thorax.55.2.170.
Xanthoma disseminatum (XD) is a rare mucocutaneous xanthomatosis classified as a benign form of non-Langerhans' cell histiocytosis. The case history is presented of a 61 year old woman with XD who developed dyspnoea and spirometric features of airflow obstruction. Bronchoscopy and computed tomography confirmed involvement of the large and medium sized bronchi and she subsequently died from acute respiratory failure. The post-mortem findings and the importance of respiratory tract disease in this unusual condition are discussed.
播散性黄瘤（XD）是一种罕见的皮肤黏膜黄瘤病，归类为非朗格汉斯细胞组织细胞增生症的一种良性形式。本文介绍了一名61岁患有播散性黄瘤的女性病例，该患者出现呼吸困难及气流受限的肺功能检查特征。支气管镜检查和计算机断层扫描证实大中型支气管受累，她随后死于急性呼吸衰竭。本文讨论了尸检结果以及呼吸道疾病在这种罕见病症中的重要性。
Zotero 插件