Maccioni F, Della Rocca C, Salvi P F, Manicone A M, Ascarelli A, Longo F, Rossi P
Department of Radiology, University of Rome La Sapienza, Policlinico Umberto I, Italy.
Abdom Imaging. 2000 Jan-Feb;25(1):103-6. doi: 10.1007/s002619910021.
Malignant peripheral neuroectodermal tumors (MPNETs) are primitive neuroblastic tumors that arise, unlike neuroblastomas, outside the autonomic nervous system. A renal origin has been described in very few cases.
We report the case of a young male patient with a large MPNET of the right kidney, studied with ultrasound and computed tomography before surgical resection. The main radiologic features, the microscopic appearance and the typical immunohistochemical findings, are described and discussed.
恶性外周神经外胚层肿瘤（MPNETs）是一种原始神经母细胞瘤，与神经母细胞瘤不同，它起源于自主神经系统之外。仅有极少数病例报道其起源于肾脏。
我们报告了一名年轻男性患者，其右肾有一个巨大的MPNET，在手术切除前接受了超声和计算机断层扫描检查。描述并讨论了主要的放射学特征、显微镜下表现及典型的免疫组化结果。
