Radiodiagnosis, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, India.
Radiodiagnosis, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, India
BMJ Case Rep. 2020 Oct 4;13(10):e235484. doi: 10.1136/bcr-2020-235484.
Primitive neuroectodermal tumour (PNET) of renal capsule is a rare entity. We report a case of a 17-year-old girl, who presented with symptoms of epigastric and right hypochondrium pain since 1 year. She was afebrile and physical examination revealed a soft, non-tender, firm, bimanually palpable and ballotable mass along right flank. Ultrasound abdomen showed a large heteroechoic mass in right suprarenal region with indistinct planes with upper pole of right kidney. On CT, a large right suprarenal mass was noted with origin likely from right adrenal gland. Surgery was done and intraoperatively, the large mass in right suprarenal region showed involvement of the upper pole of the right kidney. The right adrenal gland was small in size, compressed and displaced by the lesion. Histopathology revealed the mass to be PNET of kidney. We report the relevant imaging findings of the case with review of literature of this entity.
肾包膜原始神经外胚层肿瘤(PNET)较为罕见。我们报告了一例 17 岁女孩的病例,其自 1 年前开始出现上腹和右季肋部疼痛的症状。患者无发热,体格检查发现右侧肋弓下可触及一质软、无触痛、质硬、可双手触及的囊性感肿块。腹部超声显示右肾上腺区有一混杂回声的巨大肿块,与右肾上极分界不清。CT 示右肾上腺区有一巨大肿块,起源可能来自右侧肾上腺。行手术治疗,术中发现右肾上腺区的巨大肿块累及右肾上极。右侧肾上腺较小,被病变压迫并移位。组织病理学显示该肿块为肾 PNET。我们报告了该病例的相关影像学表现,并对该实体的文献进行了复习。