Romero-Menor C, López-Gómez D, Iráculis E, García F, Sabaté X, Esplugas E
Servicio de Cardiología, Ciutat Sanitària i Universitària de Bellvitge, L'Hospitalet de Llobregat, Barcelona.
Rev Esp Cardiol. 1999 Dec;52(12):1157-8.
Cardiac injury is a frequent characteristic in primary, senile and myeloma related amyloidosis, but it is unusual in secondary amyloidosis. We report a patient with complete atrioventricular block and polymorphic ventricular tachycardia as the initial manifestation of secondary amyloidosis. Necropsy demonstrated amyloidosis deposits in the specific conduction system.
心脏损伤是原发性、老年性和骨髓瘤相关性淀粉样变性的常见特征,但在继发性淀粉样变性中并不常见。我们报告一例以完全性房室传导阻滞和多形性室性心动过速为继发性淀粉样变性初始表现的患者。尸检显示在特定传导系统中有淀粉样变性沉积物。