Gürgün C, Sagcan A, Cinar C S, Yagdi T, Zoghi M, Tekten T, Kultursay H
Department of Cardiology, Ege University, Izmir, Turkey.
Blood Coagul Fibrinolysis. 2000 Jan;11(1):107-10.
Behçet's disease is a chronic multi-system disease presenting with recurrent oral and genital ulceration, and relapsing uveitis. Cardiac involvement is an extremely rare manifestation of this disorder. We report an unusual case of Behçet's disease characterized by a mural cardiac thrombi in the right atrium and right ventricle along with transient protein C and S deficiency.
白塞病是一种慢性多系统疾病,表现为复发性口腔和生殖器溃疡以及复发性葡萄膜炎。心脏受累是这种疾病极为罕见的一种表现。我们报告了一例罕见的白塞病病例,其特征为右心房和右心室壁内血栓形成,并伴有短暂性蛋白C和蛋白S缺乏。