Soulami S, Nour-Eddine M, Azzouzi L, Bennis A, Chraibi N
Centre de cardiologie, CHU Ibn Rochd, Casablanca, Maroc.
Arch Mal Coeur Vaiss. 1996 Jul;89(7):917-21.
Cardiac involvement is rare in Behçet's disease. Endomyocardial fibrosis of the right heart is exceptionally rare and is associated with right ventricular thrombosis. The authors report the case of a 27 year old man who died of a massive pulmonary embolism and who suffered from right-sided endomyocardial fibrosis with intraventricular thrombi. The diagnosis was made at autopsy. Behçet's disease was diagnosed on the finding of bipolar aphthous ulcers and skin hypersensitivity. The authors support previous workers in stating that Behçet's disease should be considered as a possible cause of endomyocardial fibrosis of the right heart.
心脏受累在白塞病中较为罕见。右心内膜心肌纤维化极为罕见，且与右心室血栓形成有关。作者报告了一例27岁男性病例，该患者死于大面积肺栓塞，患有右侧心内膜心肌纤维化并伴有心室内血栓形成。诊断是在尸检时做出的。根据双相性阿弗他溃疡和皮肤超敏反应的发现诊断为白塞病。作者支持之前研究者的观点，即白塞病应被视为右心内膜心肌纤维化的可能病因。
