Cruz-Velarde J A, Muñoz L, Rodrigálvarez R, Grandas F
Servicio de Neurología, Hospital General Universitario Gregorio Marañón, Madrid.
Neurologia. 2000 Jan;15(1):32-4.
A case of gliomatosis cerebri which clinically presented with a syndrome of intracranial hypertension (ICH), involvement of bilateral sixth cranial nerves, and oppressive holocranial headache of one week of evolution. Cranial MR and CT were performed demonstrating diffuse hypodense cortical-subcortical lesions on tomography and in T1 sequences and hyperdense lesions in T2 sequences with irregular contrast enhancement. Intracranial pressure was measured by ventricular catheter with the appearance of high, maintained pressure waves (Lundberg A waves). Ventricular LCR study and cerebral angiography did not provide additional data. Meningeal and cerebral biopsies showed infiltration by pleomorphous glioma leading to the diagnosis of gliomatosis cerebri. The patient was treated with steroids, hyperosmolar agents, external LCR derivation and tumoral radiotherapy. Nonetheless, the patient dies at six months of initiation of the symptoms. Gliomatosis cerebri should be taken into account in the differential diagnosis of clinical pictures presenting with ICH.
一例大脑胶质瘤病,临床表现为颅内高压综合征(ICH)、双侧第六对脑神经受累以及病程一周的进行性全颅压迫性头痛。进行了头颅磁共振成像(MR)和计算机断层扫描(CT),结果显示在断层扫描和T1序列上有弥漫性低密度皮质 - 皮质下病变,在T2序列上有高密度病变,并伴有不规则对比增强。通过脑室导管测量颅内压,出现高的、持续的压力波(伦德伯格A波)。脑室引流脑脊液(LCR)研究和脑血管造影未提供更多数据。脑膜和脑活检显示多形性胶质瘤浸润,从而诊断为大脑胶质瘤病。患者接受了类固醇、高渗剂、外部LCR引流和肿瘤放疗治疗。尽管如此,患者在症状出现六个月后死亡。在伴有ICH的临床症状鉴别诊断中应考虑大脑胶质瘤病。