Caird J, McDermott M, Farrell M
Department of Neuropathology, Beaumont Hospital, Dublin, Ireland.
Brain Pathol. 2000 Apr;10(2):317-9. doi: 10.1111/j.1750-3639.2000.tb00206.x.
A 5 month old boy was found by his mother to have a bony mass behind the left ear which extended intracranially on MRI scan. At surgery it was entirely extradural in location. Microscopically, a biphasic appearance consisting of large pigmented cells arranged into tubules and small nonpigmented basophilic cells arranged into nests gave rise to a diagnosis of melanotic neuroectodermal tumour of infancy [MNETI]. One year after a wide local excision the patient is tumor-free and developing normally. The prognosis for MNETI in general is excellent with no requirement for additional radiotherapy or chemotherapy.
一名5个月大的男婴被母亲发现左耳后方有一骨性肿物，磁共振成像（MRI）扫描显示该肿物向颅内延伸。手术时发现其完全位于硬膜外。显微镜下，肿物呈现双相外观，由排列成小管状的大色素细胞和排列成巢状的小非色素嗜碱性细胞组成，据此诊断为婴儿黑色素性神经外胚层肿瘤（MNETI）。广泛局部切除术后一年，患儿无肿瘤且发育正常。总体而言，MNETI的预后极佳，无需额外的放疗或化疗。
