肺气肿与肝脏疾病。发生于一名α-抗胰蛋白酶缺乏的成年人。
Pulmonary emphysema and liver disease. Occurrence in an alpha-antitrypsin-deficient adult.
作者信息
Donlan C J, Ross D G, Golembieski M, Scutero J V
出版信息
JAMA. 1975 Jun 16;232(11):1147-9.
PMID:1079880
Abstract
An elderly woman manifested both pulmonary and hepatic disease secondary to alpha 1-antitrypsin deficiency. The liver biopsy specimen showed the characteristic findings of this condition, most importantly, the presence of PAS-positive, diastase-resistant intracytoplasmic inclusions.
摘要
一位老年女性因α1-抗胰蛋白酶缺乏继发出现肺部和肝脏疾病。肝脏活检标本显示了该病症的特征性表现，最重要的是，存在PAS阳性、淀粉酶抵抗性胞浆内包涵体。
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