Döring L, Graudins J
Thoraxchir Vask Chir. 1975 Dec;23(6):560-6. doi: 10.1055/s-0028-1097028.
Primary hemangiopericytoma of the lung is exceedingly rare. The following characteristics were found in a survey of the 34 cases published so far in the world literature and in one case of our own, a 29 year old man with this mesenchymal tumor. It does not show specific clinical signs. In radiographs an isolated round unidentifiable focus is seen. The differential diagnosis has to rely on the histology. About one half of these tumors are discovered by accident. It appears that it occurs at a somewhat younger age in men than in women. Both sexes are equally represented. The treatments of choice are either lobectomy or pneumonectomy. Patients with small tumors without clinical signs appear to have a better prognosis. When recurrence or metastases develop they will be noticed within a few months. Intensive follow-up of patients operated on is essential, since histology cannot provide safe criteria on which one could decide whether the tumor was benign or malignant.
原发性肺血管外皮细胞瘤极为罕见。在对世界文献中迄今发表的34例病例以及我们自己遇到的1例病例（一名患有这种间叶性肿瘤的29岁男性）进行的调查中发现了以下特征。它没有特异性的临床症状。在X线片上可见一个孤立的圆形、无法明确的病灶。鉴别诊断必须依靠组织学检查。这些肿瘤约有一半是偶然发现的。似乎男性发病年龄比女性稍小。男女发病率相当。首选的治疗方法是肺叶切除术或全肺切除术。没有临床症状的小肿瘤患者预后似乎较好。当复发或转移发生时，会在几个月内被发现。对接受手术的患者进行密切随访至关重要，因为组织学检查无法提供安全的标准来判断肿瘤是良性还是恶性。
