Corrado G, Santarone M, Miglierina E, Beretta S, Frattini T, Tadeo G, Manzillo G F, Tagliagambe L M
Department of Cardiology, Valduce Hospital, Como, Italy.
Ital Heart J. 2000 May;1(5):372-5.
Noncompaction of the ventricular myocardium is a rare congenital disorder characterized by the presence of numerous prominent trabeculations and deep intertrabecular recesses which communicate with the left ventricular cavity. The disease uniformly affects the left ventricle, sometimes also affecting the right ventricle. Noncompaction of the ventricular myocardium is believed to be a disorder of endomyocardial embryogenesis. Familial occurrence has been observed. It may be accompanied by depressed ventricular function, cardiac arrhythmia and systemic embolism. Although noncompaction of the ventricular myocardium is a congenital myocardial disorder, the onset of symptoms is frequently delayed until adulthood. We describe a case of noncompaction of the ventricular myocardium in a 33-year-old male with the typical echocardiographic and cardiac magnetic resonance imaging features of this disease.
心室心肌致密化不全是一种罕见的先天性疾病，其特征是存在许多突出的肌小梁和与左心室腔相通的深肌小梁间隐窝。该疾病均累及左心室，有时也会累及右心室。心室心肌致密化不全被认为是心内膜胚胎发生的一种疾病。已观察到家族性发病情况。它可能伴有心室功能减退、心律失常和全身栓塞。虽然心室心肌致密化不全是一种先天性心肌疾病，但症状的发作通常会延迟至成年期。我们描述了一名33岁男性心室心肌致密化不全的病例，该病例具有这种疾病典型的超声心动图和心脏磁共振成像特征。
