Freeman H J, Weinstein W W, Shnitka T K, Crockford P M, Herbert F A
Ann Intern Med. 1976 Jul;85(1):73-6. doi: 10.7326/0003-4819-85-1-73.
A 39-year-old woman with homozygous ZZ alpha1-antitrypsin deficiency was found to have pancreatic fibrosis in addition to the recognized pulmonary and hepatic abnormalities. Pancreatic exocrine function was normal but endocrine studies showed glucose intolerance. Pancreatic fibrosis may be another manifestation of alpha1-antitrypsin deficiency.
一名39岁的纯合子ZZ型α1-抗胰蛋白酶缺乏症女性,除了已确认的肺部和肝脏异常外,还被发现患有胰腺纤维化。胰腺外分泌功能正常,但内分泌研究显示存在葡萄糖不耐受。胰腺纤维化可能是α1-抗胰蛋白酶缺乏症的另一种表现形式。