Utermann S, Kahle B, Petzoldt D
Hautklinik der Ruprecht-Karls-Universität Heidelberg.
Hautarzt. 2000 May;51(5):336-9. doi: 10.1007/s001050051128.
The Stewart-Bluefarb syndrome is defined as an unilateral angiodermatitis due to multiple arterio-venous fistules accompanied by acroangiodermatitis resembling Kaposi sarcoma (pseudo-kaposi sarcoma). The acroangiodermatitis is most common on the lower limb. It leads to ulcerated nodules with a high risk of bleeding and infection, as well as edema, pain and seldom limb hypertrophy. Curative therapy requires elimination of the arteriovenous shunts. Surgical destruction of the multiple small fistulae is a limitating factor. A better alternative is embolisation, but this approach carries the risk of ischemia and necrosis. A 32 year old female patient with Stewart-Bluefarb syndrome is presented; she has been successfully treated with embolisation on eight occasions.
斯图尔特 - 布卢法布综合征的定义为:因多发性动静脉瘘引起的单侧血管性皮炎,并伴有类似卡波西肉瘤的肢端血管性皮炎(假卡波西肉瘤)。肢端血管性皮炎最常见于下肢。它会导致溃疡性结节,有出血和感染的高风险,以及水肿、疼痛,很少出现肢体肥大。根治性治疗需要消除动静脉分流。手术破坏多个小瘘管是一个限制因素。更好的替代方法是栓塞,但这种方法有缺血和坏死的风险。本文介绍了一名32岁患有斯图尔特 - 布卢法布综合征的女性患者;她已成功接受了8次栓塞治疗。