Raboei E, Luoma R
Department of Pediatric Surgery, King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia.
Eur J Pediatr Surg. 2000 Apr;10(2):130-2. doi: 10.1055/s-2008-1072341.
Primary neonatal cricopharyngeal achalasia due to a spastic cricopharyngeus muscle manifests itself with intractable feeding difficulties, nasal reflux, recurrent aspiration pneumonia and failure to thrive. There are very few reports of this condition in the literature. In the absence of anatomically demonstrable cause, these children are likely to be labelled as having an impairment of the central-nervous system. This in turn may result in long-term misery with ng-tube feeding, and eventually, the creation of a feeding gastrostomy. A minor operation-- cricopharyngeal myotomy-- has been shown to be safe and curative. It can be performed even if only limited preoperative diagnostic tools are available.
原发性新生儿环咽失弛缓症是由环咽肌痉挛引起的，表现为顽固性喂养困难、鼻反流、反复吸入性肺炎和生长发育迟缓。文献中关于这种疾病的报道非常少。在没有解剖学上可证实的病因的情况下，这些儿童可能会被诊断为中枢神经系统受损。这反过来可能导致长期通过鼻饲管喂养的痛苦，最终还可能需要进行胃造瘘术。一项小手术——环咽肌切开术——已被证明是安全有效的。即使术前仅有有限的诊断工具，也可以进行该手术。
