Korakaki Eftichia, Hatzidaki Eleftheria, Manoura Antonia, Velegrakis Georgios, Charissis Georgios, Gourgiotis Dimitrios, Giannakopoulou Christina
Department of Neonatology, University of Crete, Crete, Greece.
Int J Pediatr Otorhinolaryngol. 2004 Feb;68(2):249-53. doi: 10.1016/j.ijporl.2003.10.008.
Primary cricopharyngeal achalasia resulting from failure of relaxation of the cricopharyngeus muscle is a rare but significant cause of dysphagia in newborns. Symptoms may be nonspecific. Although surgical management with cricopharyngeal myotomy has been employed successfully for the treatment of this disorder, swallowing difficulties may persist postoperatively, probably due to association with other esophageal abnormalities. Alternative methods of feeding may be required to ensure adequate nutrient intake. We report the case of a full-term, 2-day-old neonate with this rare clinical condition, treated by myotomy, in whom swallowing difficulties persisted for several weeks after surgery. Satisfactory nutrition was maintained postoperatively with the support of a nasogastric feeding tube until improvement in feeding intolerance. Complete symptomatic relief was attained at the age of 5 months.
由环咽肌松弛失败导致的原发性环咽肌失弛缓症是新生儿吞咽困难的罕见但重要原因。症状可能不具特异性。尽管环咽肌切开术的手术治疗已成功用于治疗这种疾病，但吞咽困难可能在术后持续存在，这可能是由于与其他食管异常有关。可能需要采用替代喂养方法以确保充足的营养摄入。我们报告了一例患有这种罕见临床病症的足月2日龄新生儿，通过肌切开术进行治疗，术后吞咽困难持续了数周。在鼻胃饲管的支持下，术后维持了满意的营养状况，直至喂养不耐受情况改善。5个月大时症状完全缓解。
