骨弥漫性淋巴管瘤病

Diffuse lymphangiomatosis of bone.

作者信息

Maki D D, Nesbit M E, Griffiths H J

机构信息

Department of Radiology, Hospital of the University of Pennsylvania, Philadelphia, USA.

出版信息

Australas Radiol. 1999 Nov;43(4):535-8. doi: 10.1046/j.1440-1673.1999.00726.x.

DOI:10.1046/j.1440-1673.1999.00726.x

PMID:10901976

Abstract

Two cases of lymphangiomatosis of bone, a very rare systemic condition characterized by both skeletal and parenchymal lesions, are presented. The skeletal changes have an appearance similar to haemangiomas in the spine, and soap-bubbly lesions in the flat bones. One case carried the diagnosis of eosinophilic granuloma for 18 years. The findings on MRI, which have not been previously well-established, are discussed.

摘要

本文报告了两例骨淋巴管瘤病，这是一种非常罕见的全身性疾病，其特征为骨骼和实质脏器均有病变。骨骼改变的表现类似于脊柱血管瘤以及扁骨中的皂泡样病变。其中一例曾被诊断为嗜酸性肉芽肿达18年之久。文中还讨论了此前尚未明确的磁共振成像（MRI）表现。