Barshack I, Schiby G, Shpilberg O, Sidi Y
Pathology Dept., Chaim Sheba Medical Center, Tel Hashomer.
Harefuah. 1998 Feb 15;134(4):263-5, 335.
A 48-year-old man presented with recurrent syncope which was preceded by facial edema and difficulty in breathing. Physical examination, laboratory tests, abdominal CT and bone scan were all within normal limits. Bone marrow biopsy was consistent with mastocytosis. Systemic mastocytosis consists of a spectrum of disorders characterized by aberrant proliferation of tissue mast cells, and are mainly related to mast cell mediator release.
一名48岁男性出现反复晕厥，发作前有面部水肿和呼吸困难。体格检查、实验室检查、腹部CT和骨扫描均在正常范围内。骨髓活检结果符合肥大细胞增多症。系统性肥大细胞增多症是一系列以组织肥大细胞异常增殖为特征的疾病，主要与肥大细胞介质释放有关。
