Canneto B, Carretta A, Vagani A, Puglisi A, Pansera M, Zannini P
Istituto Scientifico H San Raffaele, Università degli Studi, Milano.
Minerva Chir. 2000 May;55(5):353-6.
Due to the severity of respiratory symptoms, congenital lobar emphysema often requires surgical treatment in the early stages of life. Diagnosis of congenital lobar emphysema in adult life is therefore unusual, often presenting with mild symptoms. Diagnostic assessment is therefore of great importance in the treatment of these patients. A case of congenital lobar emphysema in an adult is reported and the diagnostic and therapeutical approach are discussed. The use of new diagnostic techniques such as dynamic RMN and SPET V/Q lung scan may improve the accuracy of the diagnostic evaluation. Pulmonary lobectomy led to marked improvement in respiratory function. Accurate diagnosis and appropriate management of congenital lobar emphysema in adult patients can lead to favourable results.
由于呼吸症状的严重性,先天性大叶性肺气肿通常在生命早期就需要手术治疗。因此,在成人期诊断先天性大叶性肺气肿并不常见,通常表现为轻微症状。所以,诊断评估在这些患者的治疗中非常重要。本文报告了一例成人先天性大叶性肺气肿病例,并讨论了其诊断和治疗方法。使用动态磁共振成像(RMN)和单光子发射计算机断层扫描(SPET)肺通气/灌注扫描等新的诊断技术可能会提高诊断评估的准确性。肺叶切除术使呼吸功能得到显著改善。准确诊断并适当处理成人先天性大叶性肺气肿患者可取得良好效果。