Martins R S, Moraes O, Siqueira M G
Centro Integrado de Neurocirurgia, Hospital Beneficência Portuguesa, São Paulo, SP, Brasil.
Arq Neuropsiquiatr. 2000 Sep;58(3A):760-3. doi: 10.1590/s0004-282x2000000400028.
Intraspinal dermoid tumor and diastematomyelia is a rare combination of pathologies and only eight cases were priorly published. We report a new case in an adult with clinical presentation of progressive paresis and sensitive deficit in the lower limbs, associated with a thoraco-lombar kyphoscoliosis. The diagnosis based on the CT scan and MR images was confirmed at surgery. Pathophysiologic and clinical aspects as well as the radiological characteristics of these pathologies are dicussed and the importance of the early diagnosis is emphasized.
脊髓内皮样囊肿合并脊髓纵裂是一种罕见的病理组合,此前仅有8例报道。我们报告一例成年患者的新病例,其临床表现为进行性下肢轻瘫和感觉障碍,并伴有胸腰段脊柱后凸侧弯。基于CT扫描和磁共振成像的诊断在手术中得到证实。本文讨论了这些病症的病理生理和临床方面以及放射学特征,并强调了早期诊断的重要性。