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Common variable immunodeficiency (CVID) and inclusion body myositis (IBM).

作者信息

Gause A, Inderrieden D C, Laas R, Arlt A C, Gross W L

机构信息

Poliklinik für Rheumatologie, Universitätsklinikum Lübeck und Krankenhausabteilung der Rheumaklinik Bad Bramstedt, Germany.

出版信息

Immunobiology. 2000 Aug;202(2):199-203. doi: 10.1016/S0171-2985(00)80067-4.

DOI:10.1016/S0171-2985(00)80067-4
PMID:10993295
Abstract

A case of a 38-year old man with a common variable immunodeficiency syndrome (CVID) is demonstrated who suffered at the same time from a histologically proven inclusion body myositis (IBM). The myositis did not resolve after institution of regular intravenous IgG infusions. This case demonstrates a very long lasting benign course of IBM. The occurrence with CVID may be a clinical hint for a viral pathogenesis of IBM. So far only two similar cases are reported in the literature.

摘要

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