Puri V, Garg N, Kumar N, Tatke M
Departments of Neurology and Pathology, G.B. Pant Hospital, New Delhi, 110002, India.
Neurol India. 2000 Sep;48(3):263-5.
A 53 years old male, a known case of ankylosing spondylitis having recurrent attacks of hypoglycaemia, developed symmetrical distal sensorimotor neuropathy. The neuropathy was axonal with secondary demyelination. Evidence of vasculopathy was also noted on histopathology of the nerve. Serum C-peptide level was low, a feature reported with autoimmune hypoglycaemia with antireceptor antibodies. The patient showed spontaneous recovery.
一名53岁男性,已知患有强直性脊柱炎且反复出现低血糖发作,发展为对称性远端感觉运动性神经病变。该神经病变为轴索性伴继发性脱髓鞘。在神经组织病理学检查中也发现了血管病变的证据。血清C肽水平较低,这是抗受体抗体所致自身免疫性低血糖的一个特征。该患者出现了自发恢复。