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特发性眼部神经肌强直:一种神经血管压迫综合征?

Idiopathic ocular neuromyotonia: a neurovascular compression syndrome?

作者信息

Tilikete C, Vial C, Niederlaender M, Bonnier P L, Vighetto A

机构信息

Neuro-ophthalmology Unit, Hôpital Neurologique et Neurochirurgical P Wertheimer, 59 Bd Pinel, 69003 Lyon, France.

出版信息

J Neurol Neurosurg Psychiatry. 2000 Nov;69(5):642-4. doi: 10.1136/jnnp.69.5.642.

DOI:10.1136/jnnp.69.5.642
PMID:11032618
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1763409/
Abstract

Ocular neuromyotonia in the muscles innervated by the right oculomotor nerve was diagnosed in a patient without a history of radiation therapy. Electromyography of the levator palpebrae showed continuous motor unit activity. Brain MRI disclosed a close contact between the right third cranial nerve and a basilar artery dolichoectasia. The patient partly benefited from carbamazepine therapy. This unique finding suggests that neurovascular compression syndrome could be an hitherto unrecognised cause of ocular neuromyotonia.

摘要

一名无放疗史的患者被诊断为右侧动眼神经支配肌肉的眼性神经肌强直。上睑提肌肌电图显示运动单位持续活动。脑部磁共振成像显示右侧第三脑神经与基底动脉延长扩张症紧密接触。患者从卡马西平治疗中部分获益。这一独特发现提示神经血管压迫综合征可能是迄今未被认识的眼性神经肌强直病因。