Yürüten Betigül, Ilhan Süleyman
Department of Neurology, School of Medicine, Selçuk University, 42080 Konya, Turkey.
Clin Neurol Neurosurg. 2003 Apr;105(2):140-2. doi: 10.1016/s0303-8467(02)00138-5.
Ocular neuromyotonia is a rare clinical entity, which is characterized by spontaneous spasm of ocular muscles resulting in paroxysmal diplopia and strabismus. Inappropriate discharges from ocular motor neurons or axons with unstable cell membranes may cause the sustained contraction of their respective ocular muscles. In most cases, ocular neuromyotonia resulted from radiation therapy to the parasellar and sellar regions or compressive lesions on ocular motor nerves. Among 30 patients reported in the literatür only six patients were accepted as idiopathic. Here, we reported a patient with third nerve myotonia representing with spells of diplopia. No lesion was found and she was accepted as idiopathic ocular neuromyotonia.
眼肌神经性肌强直是一种罕见的临床病症,其特征为眼肌自发痉挛,导致阵发性复视和斜视。眼运动神经元或细胞膜不稳定的轴突的不适当放电可能导致其各自眼肌的持续收缩。在大多数情况下,眼肌神经性肌强直是由鞍旁和鞍区的放射治疗或眼运动神经的压迫性病变引起的。在文献报道的30例患者中,只有6例被认为是特发性的。在此,我们报告了一例以复视发作为表现的动眼神经肌强直患者。未发现病变,她被诊断为特发性眼肌神经性肌强直。