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一名成年患者出现室性心律失常,诊断为心脏横纹肌瘤。

Cardiac rhabdomyoma in an adult patient presenting with ventricular arrhythmia.

作者信息

Krasuski R A, Hesselson A B, Landolfo K P, Ellington K J, Bashore T M

机构信息

Division of Cardiology, Duke University Medical Center, Durham, NC, USA.

出版信息

Chest. 2000 Oct;118(4):1217-21. doi: 10.1378/chest.118.4.1217.

Abstract

Cardiac rhabdomyomas are extremely uncommon in the adult patient. We describe a previously healthy man who presented with ventricular arrhythmias resulting from a right ventricular, cardiac rhabdomyoma. Echocardiography, CT scanning, and MRI are recognized as useful diagnostic modalities for intracardiac lesions. Cardiac catheterization in our patient demonstrated the presence of a tumor blush. This has not previously been reported with cardiac rhabdomyomas. Although lesions may spontaneously regress, surgery is often necessary and frequently resolves the underlying arrhythmia.

摘要

心脏横纹肌瘤在成年患者中极为罕见。我们描述了一名既往健康的男性,他因右心室心脏横纹肌瘤出现室性心律失常。超声心动图、CT扫描和MRI被认为是诊断心内病变的有用方法。我们患者的心脏导管检查显示有肿瘤染色。此前心脏横纹肌瘤尚未有此报道。尽管病变可能会自发消退,但手术往往是必要的,且常常能解决潜在的心律失常问题。

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