Casey M, Radel E, Ratech H
Department of Pathology, Albert Einstein College of Medicine/Montefiore Medical Center, Bronx, New York 10467, USA.
J Pediatr Hematol Oncol. 2000 Sep-Oct;22(5):468-71. doi: 10.1097/00043426-200009000-00018.
Churg-Strauss syndrome is a systemic vasculitis characterized by asthma, tissue and blood eosinophilia, and granulomatous vasculitis. Lymph node involvement as part of systemic disease or as the primary site of involvement is rare. We report a single case of primary (isolated) nodal Churg-Strauss syndrome occurring in an 11-year-old boy with asthma, fever, night sweats, and cervical adenopathy. The clinical diagnosis was lymphoma. The unusual presentation of Churg-Strauss syndrome limited to lymph nodes is important to recognize and diagnose correctly because the administration of steroid therapy is associated with a favorable outcome.
变应性肉芽肿性血管炎是一种系统性血管炎，其特征为哮喘、组织和血液嗜酸性粒细胞增多以及肉芽肿性血管炎。作为全身性疾病一部分或作为主要受累部位的淋巴结受累情况罕见。我们报告了一例原发性（孤立性）淋巴结变应性肉芽肿性血管炎病例，发生在一名11岁男孩身上，该男孩有哮喘、发热、盗汗和颈部淋巴结病。临床诊断为淋巴瘤。认识并正确诊断局限于淋巴结的变应性肉芽肿性血管炎的不寻常表现很重要，因为给予类固醇治疗会带来良好预后。
