Esquivel J, Sugarbaker P H
Washington Cancer Institute, Washington Hospital Center, Washington, DC, USA.
Br J Surg. 2000 Oct;87(10):1414-8. doi: 10.1046/j.1365-2168.2000.01553.x.
Pseudomyxoma peritonei syndrome is characterized by a gradual expansion of mucoid tumour and fluid at specific sites within abdominopelvic regions as a result of a perforated appendiceal adenoma. The aim was to analyse the presenting symptoms and signs of patients with this condition.
Of 410 patients with appendiceal tumours 217 had the diagnosis of pseudomyxoma peritonei syndrome with histological confirmation. A retrospective review of the clinical characteristics that determine presentation was performed.
Overall, suspected acute appendicitis was the most common presentation (27 per cent). For women the diagnosis was most commonly made while being evaluated for an ovarian mass (39 per cent). Increasing abdominal girth was the second most common presentation overall (23 per cent). Thirty patients (14 per cent) presented with new-onset hernia, of which the majority (26) were inguinal hernias.
Consideration of appendicitis, increased abdominal girth, ovarian mass and new-onset hernia as caused by this syndrome may facilitate diagnosis and definitive treatment.
腹膜假黏液瘤综合征的特征是阑尾腺瘤穿孔导致黏液性肿瘤和液体在腹盆腔特定部位逐渐扩张。目的是分析患有这种疾病的患者的症状和体征。
在410例阑尾肿瘤患者中，217例经组织学证实诊断为腹膜假黏液瘤综合征。对决定临床表现的临床特征进行了回顾性分析。
总体而言，疑似急性阑尾炎是最常见的表现（27%）。对于女性患者，最常见的诊断是在评估卵巢肿块时做出的（39%）。腹围增加是总体上第二常见的表现（23%）。30例患者（14%）出现新发疝，其中大多数（26例）为腹股沟疝。
将由该综合征引起的阑尾炎、腹围增加、卵巢肿块和新发疝纳入考虑，可能有助于诊断和确定性治疗。
