Keppy D O, Denell R E
Genetics. 1979 Mar;91(3):421-41. doi: 10.1093/genetics/91.3.421.
The extensive analysis of the impact of segmental aneuploidy by Lindsley et al. (1972) showed that there are relatively few haplo-lethal loci in the genome and that, with one exception, all loci are triplo-viable. The exceptional locus, which lies in salivary gland chromosome region 83D-E, is associated with lethality when present in either one or three doses in an otherwise diploid individual (Denell 1976). The genetic nature of the phenomenon has been studied by examining the rates of induction, by ionizing radiation and chemical mutagens, of mutations affecting the dose-sensitive behavior. For both types of mutagens, the frequency of inactivation of the locus is relatively low, and a high proportion of such mutations is associated with chromosomal deficiencies. These data indicate that the locus is infrequently and perhaps never inactivated by a DNA base-pair substitution and thus that the triplo-lethal phenomenon is not associated with a "typical" structural gene. It is possible that the triplo-lethal locus is very small, is reiterated or otherwise complex or is functionally insensitive to base-pair substitutions. The result that all mutations that complement a duplication of the triplo-lethal locus are lethal in heterozygous combination with a normal third chromosome argues that triplo- and haplo-lethality are concomitants of the same phenomenon. Salivary gland chromosome analysis of newly induced deficiencies and duplications localizes the locus to 83D4,5--83E1,2, and further cytogenetic mapipulation shows that the dose-sensitive behavior is independent of the position of the locus in the genome.
林兹利等人(1972年)对染色体节段非整倍体影响的广泛分析表明,基因组中半合子致死基因座相对较少,并且除一个例外,所有基因座在三倍体状态下都是可行的。这个例外的基因座位于唾液腺染色体区域83D - E,当在其他方面为二倍体的个体中以单剂量或三剂量存在时会导致致死(德内尔,1976年)。通过检测电离辐射和化学诱变剂诱导影响剂量敏感行为的突变率,对该现象的遗传本质进行了研究。对于这两种诱变剂,该基因座的失活频率相对较低,并且此类突变的很大一部分与染色体缺失相关。这些数据表明,该基因座很少(也许从未)因DNA碱基对替换而失活,因此三倍体致死现象与“典型”结构基因无关。三倍体致死基因座可能非常小、是重复的或其他复杂的,或者对碱基对替换在功能上不敏感。所有与三倍体致死基因座重复互补的突变在与正常第三条染色体的杂合组合中都是致死的,这一结果表明三倍体致死和半合子致死是同一现象的伴随情况。对新诱导的缺失和重复进行唾液腺染色体分析,将该基因座定位到83D4,5 - 83E1,2,进一步的细胞遗传学操作表明剂量敏感行为与该基因座在基因组中的位置无关。