Kaye L C, Kaye S B, Lagnado R, Boothroyd A, Morton C, May P
Royal Liverpool Children's Hospital, Alder Hey, UK.
Dev Med Child Neurol. 2000 Oct;42(10):704-6. doi: 10.1017/s0012162200001304.
A rare case of visual loss as the presenting feature of a central arteriovenous malformation involving the vein of Galen is reported. A 5-year-old girl with a history of deteriorating vision for the past 6 months was examined. Ocular examination showed a left hemianopia, left optic atrophy, and dilated vessels of the right optic disc. MRI revealed a massive deep-seated central arteriovenous malformation involving the vein of Galen. The mechanism of visual loss is likely to be a combination of ischaemic optic atrophy associated with a steal phenomenon and direct compression of the right optic radiation.