Kaye L C, Kaye S B, Lagnado R, Boothroyd A, Morton C, May P
Royal Liverpool Children's Hospital, Alder Hey, UK.
Dev Med Child Neurol. 2000 Oct;42(10):704-6. doi: 10.1017/s0012162200001304.
A rare case of visual loss as the presenting feature of a central arteriovenous malformation involving the vein of Galen is reported. A 5-year-old girl with a history of deteriorating vision for the past 6 months was examined. Ocular examination showed a left hemianopia, left optic atrophy, and dilated vessels of the right optic disc. MRI revealed a massive deep-seated central arteriovenous malformation involving the vein of Galen. The mechanism of visual loss is likely to be a combination of ischaemic optic atrophy associated with a steal phenomenon and direct compression of the right optic radiation.
报告了一例罕见病例,以视力丧失为表现特征的累及大脑大静脉的中枢动静脉畸形。对一名有过去6个月视力恶化病史的5岁女孩进行了检查。眼部检查显示左侧偏盲、左侧视神经萎缩以及右侧视盘血管扩张。磁共振成像(MRI)显示一个累及大脑大静脉的巨大深部中枢动静脉畸形。视力丧失的机制可能是与盗血现象相关的缺血性视神经萎缩和右侧视辐射直接受压的综合作用。