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肾病综合征合并轻度慢性肾衰竭时的类Purtscher样视网膜病变

Purtscher-like retinopathy in nephrotic syndrome associated with mild chronic renal failure.

作者信息

Zwolińska D, Medyńska A, Galar A, Turno A

机构信息

Department of Pediatric Nephrology, Medical University, Wrocław, Poland.

出版信息

Pediatr Nephrol. 2000 Nov;15(1-2):82-4. doi: 10.1007/s004670000411.

DOI:10.1007/s004670000411
PMID:11095019
Abstract

A sudden loss of vision attributable to Purtscher-like retinopathy occurred in a 4-year-old boy with focal segmental glomerulosclerosis and nephrotic syndrome as well as mild chronic renal failure. This retinopathy was bilateral. After treatment with intravenous methylprednisolone, infusion of 20% albumin, and low molecular weight heparin (nadroparin calcium), his visual acuity improved within 3 days. Ischemic retinal blanching and hemorrhages gradually disappeared. The pathogenesis of this disorder is unknown.

摘要

一名患有局灶节段性肾小球硬化症、肾病综合征以及轻度慢性肾衰竭的4岁男孩突然出现了类似Purtscher样视网膜病变导致的视力丧失。这种视网膜病变是双侧性的。在接受静脉注射甲泼尼龙、输注20%白蛋白以及低分子量肝素(那屈肝素钙)治疗后,他的视力在3天内得到改善。视网膜缺血性变白和出血逐渐消失。这种病症的发病机制尚不清楚。

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