假性卟啉症

Pseudoporphyria.

作者信息

Green J J, Manders S M

机构信息

Division of Dermatology, Department of Medicine, University of Medicine and Dentistry of New Jersey-Robert Wood Johnson Medical School, Camden, NJ, USA.

出版信息

J Am Acad Dermatol. 2001 Jan;44(1):100-8. doi: 10.1067/mjd.2000.111338.

DOI:10.1067/mjd.2000.111338

PMID:11148469

Abstract

Pseudoporphyria is the term used to describe a photodistributed bullous disorder with clinical and histologic features of porphyria cutanea tarda, but without accompanying biochemical porphyrin abnormalities. Medications, chronic renal failure/dialysis, excessive sun exposure and UVA radiation have all been reported to cause pseudoporphyria. Recognition, diagnosis, and appropriate management of pseudoporphyria are discussed.

摘要

假性卟啉病是用于描述一种光分布性大疱性疾病的术语，其具有迟发性皮肤卟啉病的临床和组织学特征，但无伴随的生化卟啉异常。据报道，药物、慢性肾衰竭/透析、过度日晒和紫外线A辐射均可导致假性卟啉病。本文讨论了假性卟啉病的识别、诊断及适当管理。