Aguiar T
Unidade de Neurologia, Hospital de Dona Estefânia, Lisboa.
Acta Med Port. 2000 Jul-Aug;13(4):193-8.
Subacute sclerosing panencephalitis is a slowly progressive neurodegenerative disorder occurring in childhood and adolescence and is characterised by dementia, ataxia, myoclonias and other neurological focal signs, with an invariably fatal outcome. The author reviews the subject, focussing on epidemiology, clinical features, measles virus behaviour, host immune reactions, measles prophylaxis and treatment proposals.
亚急性硬化性全脑炎是一种发生于儿童期和青春期的缓慢进展性神经退行性疾病,其特征为痴呆、共济失调、肌阵挛及其他局灶性神经体征,预后总是致命的。作者回顾了该主题,重点关注流行病学、临床特征、麻疹病毒行为、宿主免疫反应、麻疹预防及治疗建议。