Scheele J S, Ripple D, Lübbert M
Department of Medicine, University of Freiburg Medical Center, Germany.
Cell Mol Life Sci. 2000 Dec;57(13-14):1950-63. doi: 10.1007/pl00000675.
Recent progress in the understanding of signal transduction and gene regulation in hematopoietic cells has shown that many intracellular signalling pathways are modulated by low molecular weight guanine nucleotide (GTP)-binding proteins (LMWGs). LMWGs act as molecular switches for regulating a wide range of signal-transduction pathways in virtually all cells. In hematopoietic cells, LMWGs have been shown to participate in essential functions such as growth control, differentiation, cytoskeletal organization, cytokine and chemoattractant-induced signalling events, reduced nicotinamide adenine dinucleotide phosphate oxidase activity, intracellular vesicle transport and secretion. In human leukemias, myelodysplastic syndromes and myeloproliferative disorders, Ras activation occurs by point mutations, overexpression or by alteration of NF-1 Ras-GTPase activating protein (GAP). These are postinitiation events in leukemia but may modulate growth-factor-dependent and independent leukemic growth. Two animal models of mutated N-ras expression resulting in myelodysplastic and myeloproliferative features are discussed. The role of Ras in organ development is discussed in the context of transgenic knockout mice. More LMWG functions will certainly be identified as we gain a better understanding of regulatory pathways modulating myeloid signal transduction. This review will summarize our current understanding of this rapidly advancing area of research.
近年来,在造血细胞信号转导和基因调控方面的研究进展表明,许多细胞内信号通路受低分子量鸟嘌呤核苷酸(GTP)结合蛋白(LMWG)的调节。LMWG作为分子开关,在几乎所有细胞中调节广泛的信号转导通路。在造血细胞中,LMWG已被证明参与多种重要功能,如生长控制、分化、细胞骨架组织、细胞因子和趋化因子诱导的信号事件、还原型烟酰胺腺嘌呤二核苷酸磷酸氧化酶活性、细胞内囊泡运输和分泌。在人类白血病、骨髓增生异常综合征和骨髓增殖性疾病中,Ras激活通过点突变、过表达或NF-1 Ras-GTP酶激活蛋白(GAP)的改变而发生。这些是白血病中的起始后事件,但可能调节依赖生长因子和不依赖生长因子的白血病生长。本文讨论了两种因N-ras表达突变而导致骨髓增生异常和骨髓增殖特征的动物模型。在转基因敲除小鼠的背景下讨论了Ras在器官发育中的作用。随着我们对调节髓系信号转导的调控通路有更好的理解,肯定会发现更多LMWG的功能。本综述将总结我们目前对这一快速发展的研究领域的理解。