Dubois P E, Veyckemans F, Ledent M M, Michel M, de Clety S C
Department of Anaesthesia, University Clinics UCL of Mont-Godinne, B-5530 Yvoir, Belgium.
Acta Anaesthesiol Belg. 2001;52(1):21-4.
Ehlers-Danlos syndrome type VIIc is characterized by altered tensile strength of connective tissue. Several severe complications exist but skin fragility is the origin of perioperative morbidity during routine procedures. We describe the difficulties encountered during the anaesthetic management of a child suffering from the disease, and suggest special care advices to avoid any skin injury.
VIIc型埃勒斯-当洛综合征的特征是结缔组织抗张强度改变。存在几种严重并发症，但皮肤脆弱是常规手术围手术期发病的根源。我们描述了一名患有该疾病的儿童在麻醉管理过程中遇到的困难，并提出了特别护理建议以避免任何皮肤损伤。
